Double esophageal cyst is the second most common type of gastrointestinal duplication cyst, after ileal double cyst. However, less than 100 cases of double esophageal cyst are currently documented. Double esophageal cyst usually occurs alone; however, two cases of multiple (two) double esophageal cysts have been reported.

Double oesophagitis is a rare congenital malformation of the esophagus, ranking second in gastrointestinal tract diseases after ileostomy and accounting for about 15% of all congenital malformations of the esophagus. The disease is divided into 2 types: cystic double esophagus being the most common form (95%) and tubular double esophagus being very rare.