A total atrioventricular canal, also known as an atrioventricular septal defect, accounts for 2% of congenital heart diseases, and is associated with about 30% of Down's disease. In children with Down syndrome, 40% are associated with congenital hearts and 30% of congenital hearts with Down syndrome are atrioventricular canal lesions.

Atrioventricular canal is one of the congenital malformations, accounting for a high rate in congenital heart diseases. Children with a diagnosis of atrioventricular canal require early surgery to ensure proper functioning of the heart as well as the whole body.

Complete atrioventricular canal defect is a dangerous and complicated congenital heart disease that leaves many complications. Treatment needs to be done early. The specific cause of the disease is not determined, however, there are some factors related to the disease.

Children born with congenital heart disease need surgery. Atrioventricular canal is one of the congenital heart diseases and accounts for the highest rate of congenital heart disease.