Congenital biliary atresia in children is a dangerous disease that needs to be treated early. Surgery is the optimal treatment method today. After surgery, the child needs careful care to avoid biliary tract infection and increased portal vein pressure.

Chronic biliary hepatitis in congenital biliary atresia leads to progressive biliary cirrhosis, which causes portal hypertension, which may lead to venous bleeding and ascites. The development of splenomegaly or thrombocytopenia after Kasai surgery suggests the possibility of progressive portal hypertension.