Congenital cystic lung malformation: What you need to know

This is an automatically translated article.


Posted by Specialist Doctor I Dang Thi Ngoc Chuong - Pediatrician - Department of Pediatrics - Neonatology, Vinmec Central Park International General Hospital

Congenital cystic lung malformation is a rare malformation of the lower respiratory tract. The disease can leave many complications, causing children to have respiratory failure, pneumonia, wheezing, etc. Therefore, parents need to pay attention when their children have abnormal signs and need to take them quickly to medical centers. medical examination and treatment.

1. Congenital cystic lung malformation


Congenital Pulmonary Anomaly (CPAM), formerly known as Congenital Cystic Anomaly (CCAM), is a rare developmental anomaly of the lower respiratory tract. Patients may have respiratory failure in infancy or may be asymptomatic until later in life.
The disease can be detected by routine pregnancy ultrasound. Accordingly, surgical resection is the definitive treatment. Clinical symptoms will depend on the size of the cyst.
Thoracic deformity due to large cyst size. Wheezing, traction breathing, chest indrawing, cyanosis,... are early manifestations in the neonatal period: cysts are of medium size. Recurrent respiratory tract infections: late detection, infants and children: cysts are often very small. Therefore, when detecting that a child has symptoms of prolonged cough, wheezing, or recurrent pneumonia, it is necessary to take the child to a highly qualified medical facility for a doctor to check and prescribe timely treatment. to avoid possible dangerous complications.

Một số trường hợp, cha mẹ nên đưa trẻ đến gặp bác sĩ để được tư vấn và điều trị kịp thời
Một số trường hợp, cha mẹ nên đưa trẻ đến gặp bác sĩ để được tư vấn và điều trị kịp thời

2. Diagnosis of congenital lung cyst malformation


Congenital cystic lung malformation can be detected early in the fetal period by fetal ultrasound or MRI scan, detected before the 20th week. Accordingly, imaging methods will be available to the doctor. These anomalies are clearly visible:

Doppler ultrasound, MRI. Prenatal ultrasound: solid or large cystic lesion +/- hydroedema due to mediastinal displacement and inferior vena cava compression. Chest X-ray: image of homogeneous mass or cyst +/- air-fluid level. Contrast-enhanced CT scan is almost 100% sensitive, showing a homogeneous mass or cyst +/- air-fluid level. Additional screening tests for malformations that can be used are abdominal ultrasound, transfocal ultrasound. The disease can cause complications such as lung abscess (when superinfection), pneumothorax (when air capsule burst), respiratory failure, pneumonia, even more seriously, death. Therefore, parents need to pay attention to soon bring their children to medical centers for examination and treatment.

Kỹ thuật siêu âm thai có thể giúp bác sĩ chẩn đoán dị dạng nang phổi bẩm sinh
Kỹ thuật siêu âm thai có thể giúp bác sĩ chẩn đoán dị dạng nang phổi bẩm sinh

Vinmec International General Hospital is the address for receiving and examining respiratory diseases that infants and young children are susceptible to: viral fever, bacterial fever, respiratory infection, pneumonia in children, .... With modern equipment, sterile space, minimizing the impact as well as the risk of disease spread. Along with that is the dedication from the doctors with professional experience with pediatric patients, making the examination no longer a concern of the parents.

Please dial HOTLINE for more information or register for an appointment HERE. Download MyVinmec app to make appointments faster and to manage your bookings easily.

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