Cowden syndrome is a rare disorder with an incidence of 1 in 200,000. People with this syndrome often have large heads, benign tumors of the hair follicles, and white papules with a smooth surface in the mouth that begin to appear in their late 20s. Cowden syndrome is an inherited condition that is linked associated with an increased risk of breast cancer and the very common oral papilloma. So what is Cowden's syndrome? The article will find out what is Cowden's syndrome?u about this syndrome.